[1]李波,李亮,戚永发,等.82岁男性右侧肩胛部恶性外周神经鞘瘤1例[J].中国临床神经外科杂志,2024,29(03):185-186.[doi:10.13798/j.issn.1009-153X.2024.03.014]
　LI Bo,LI Liang,QI Yong-fa,et al.A rare case of an 82-year-old man with a malignant peripheral nerve sheath tumor in the right scapula[J].,2024,29(03):185-186.[doi:10.13798/j.issn.1009-153X.2024.03.014]
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82岁男性右侧肩胛部恶性外周神经鞘瘤1例()
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《中国临床神经外科杂志》[ISSN:1009-153X/CN:42-1603/TN]

卷:
29
期数:
2024年03期
页码:
185-186
栏目:
个案报道
出版日期:
2024-03-31

文章信息/Info

Title:
A rare case of an 82-year-old man with a malignant peripheral nerve sheath tumor in the right scapula
文章编号:
1009-153X（2024）03-0185-02
作者:
李波; 李亮; 戚永发; 张奇
261053山东潍坊，山东第二医科大学临床医学院（李波、戚永发、张奇）；255000山东，淄博市中心医院烧伤与创面修复外科（李亮）
Author(s):
LI Bo1;  LI Liang2;  QI Yong-fa1;  ZHANG Qi1
1. School of Clinical Medicine, Shandong Second Medical University, Weifang 261053, China; 2. Department of Burns and Wound Repair Surgery, Zibo Central Hospital, Zibo 255000, China
关键词:
恶性外周神经鞘瘤; 右侧肩部; 手术
Keywords:
Malignant peripheral nerve sheath tumor;  Right shoulder;  Surgery
分类号:
R 739.43; R 651.1+1
DOI:
10.13798/j.issn.1009-153X.2024.03.014
文献标志码:
B
摘要:
恶性外周神经鞘瘤（又称为恶性周围神经鞘瘤）是一种高度恶性神经系统肿瘤，因临床罕见，临床医生对其认识尚存在不足。本文报道1例82岁男性恶性外周神经鞘瘤，因右侧肩胛部皮肤肿物进行性增大12年入院，MRI检查发现右侧肩胛部皮下占位并明显强化，术前考虑肿瘤。完善术前准备后，一期手术完整切除肿物，二期手术植皮修复创面。术后病理诊断为恶性外周神经鞘瘤。术后5个月随访，创面愈合良好，未见肿瘤复发。恶性外周神经鞘瘤侵袭性高，局部复发率高，生存率低，因此，早发现、早治疗尤为重要，扩大切除肿瘤以保证切缘阴性是主要治疗方式。
Abstract:
Malignant peripheral nerve sheath tumor (also known as malignant peripheral nerve sheath tumor) is a highly malignant tumor of the nervous system. Because of its clinical rarity, clinicians still have insufficient understanding of it. This paper reports a case of malignant peripheral nerve sheath tumor in an 82-year-old man. He was admitted to hospital for 12 years due to progressive enlargement of a mass in the right scapula. MRI found a space occupying in the right scapula with significant enhancement, considering a tumor preoperatively. After completing preoperative preparation, the mass was completely removed in the first stage surgery, and the wound was repaired in the second stage surgery. The postoperative pathological diagnosis was malignant peripheral nerve sheath tumor. Five months after surgery, the wound healed well, and no tumor recurrence was found. Malignant peripheral nerve sheath tumor is highly invasive, with a high local recurrence rate and a low survival rate. Therefore, early detection and early treatment are particularly important. Extended resection of the tumor to ensure negative margins is the main treatment method.

参考文献/References:

[1]FYRMPAS G, BARKOULAS E. Isolated malignant peripheral nerve sheath tumor of the scalp [J]. Ear Nose Throat J, 2023, 102(3): NP104-NP105.
[2]SOMATILAKA BN, SADEK A, MCKAY RM, et al. Malignant peripheral nerve sheath tumor: models, biology, and translation [J]. Oncogene, 2022, 41(17): 2405-2421.
[3]ZHANG Y, CAI H, LV G, et al. A giant posterior mediastinal malignant peripheral nerve sheath tumor and benign neurofibroma in body surface: a case report [J]. BMC Surg, 2021, 21(1): 128.
[4]PAPARELLA MT, EUSEBI L, MAZZUCCHELLI R, et al. Lumbar malignant peripheral nerve sheath tumor: a rare case in a young patient [J]. Acta Biomed, 2022, 93(S1): e2022095.
[5]SHARMA S, SHAH JS, BALI H. Malignant peripheral nerve sheath tumor: a rare malignancy [J]. J Oral Maxillofac Pathol, 2020, 24 (Suppl 1): S86-S90.
[6]JONES KE, PATEL A, KUNESH MG, et al. Malignant peripheral nerve sheath tumor of the orbit: a case report and review of the literature [J]. Orbit, 2022, 41(5): 642-646.

备注/Memo

备注/Memo:
（2023-09-27收稿，2024-01-04修回）
通信作者：李　亮，Email：0533liliang@sina.com
更新日期/Last Update: 2024-03-31