[1]比拉力·巴拉江,阿依图尔荪·阿卜杜外力,朱国华,等.Chiari 1型畸形的诊治分析（附99例报道）[J].中国临床神经外科杂志,2023,28(03):153-155.[doi:10.13798/j.issn.1009-153X.2023.03.003]
　BILALI Balajiang,AYITUERSUN Abuduwaili,ZHU Guo-hua,et al.Diagnosis and treatment of Chiari type 1 malformation (report of 99 cases)[J].,2023,28(03):153-155.[doi:10.13798/j.issn.1009-153X.2023.03.003]
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Chiari 1型畸形的诊治分析（附99例报道）()
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《中国临床神经外科杂志》[ISSN:1009-153X/CN:42-1603/TN]

卷:
28
期数:
2023年03期
页码:
153-155
栏目:
论著
出版日期:
2023-03-31

文章信息/Info

Title:
Diagnosis and treatment of Chiari type 1 malformation (report of 99 cases)
文章编号:
1009-153X（2023）03-0153-03
作者:
比拉力·巴拉江; 阿依图尔荪·阿卜杜外力; 朱国华; 更·党木仁加甫; 汪永新
830054乌鲁木齐，新疆医科大学第一附属医院神经外科（比拉力·巴拉江、阿依图尔荪·阿卜杜外力、朱国华、更·党木仁加甫、汪永新）
Author(s):
BILALI Balajiang;  AYITUERSUN Abuduwaili;  ZHU Guo-hua;  GENG Dangmurenjiafu;  WANG Yong-xin
Department of Neurosurgery, The First Affiliated Hospital of Xinjiang Medical University, Urumqi 830054, China
关键词:
Chiari 1型畸形; 诊断; 治疗; 保守治疗; 手术
Keywords:
Chiari type 1 malformation;  Cerebellar tonsillar hernia malformation;  Diagnosis;  Surgery;  Conservative treatment
分类号:
A
DOI:
10.13798/j.issn.1009-153X.2023.03.003
文献标志码:
R742.8;R651.1+1
摘要:
目的 探讨Chiari 1型畸形（C1M）的诊断、治疗方法及其疗效。方法 回顾性分析2015年2月至2022年6月收治的99例C1M的临床资料。19例采用保守治疗组，80例采用手术治疗。所有病人随访1年。结果 保守治疗19例中，症状改善2例（10.5%），无改善16例（84.2%），恶化1例（5.3%）。手术治疗80例中，症状改善69例（86.3%），无改善10例（12.5%），术后因急性呼吸衰竭死亡1例（1.2%）。结论 C1M的诊断主要依靠临床表现及影像学表现；以手术治疗为主，疗效显著。
Abstract:
Objective To investigate the diagnosis and treatment of Chiari type 1 malformation (C1M). Methods The clinical data of 99 patients with C1M who were admitted to our hospital from February 2015 to June 2022 were retrospectively analyzed. Of 99 patients, 19 patients received conservative treatment and 80 patients received surgery. All patients were followed up for 1 year. Results Of 19 patients receiving conservative treatment, symptoms were improved in 2 patients (10.5%), not changed in 16 (84.2%), and worsened in 1 (5.3%). Of 80 patients receiving operation, symptoms were improved in 69 patients (86.3%), not changed in 10 patients (12.5%), and 1 patient (1.2%) died of acute respiratory failure. Conclusions The diagnosis of C1M mainly depends on clinical and imaging manifestations. Surgical treatment, which is more effective than conservative treatment, is the main treatment methods for C1M.

参考文献/References:

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备注/Memo

备注/Memo:
（2022-09-15收稿，2022-12-20修回）
通讯作者：汪永新，E-mail：xjdwyx2000@sohu.com
更新日期/Last Update: 2022-04-30