[1]赵国杰,刘仁忠.中枢神经系统血管母细胞瘤的诊治进展[J].中国临床神经外科杂志,2024,29(07):431-433.[doi:10.13798/j.issn.1009-153X.2024.07.010]
　ZHAO Guo-jie,LIU Ren-zhong.Progress in diagnosis and treatment of hemangioblastoma of the central nervous system[J].,2024,29(07):431-433.[doi:10.13798/j.issn.1009-153X.2024.07.010]
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中枢神经系统血管母细胞瘤的诊治进展()
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《中国临床神经外科杂志》[ISSN:1009-153X/CN:42-1603/TN]

卷:
29
期数:
2024年07期
页码:
431-433
栏目:
综述
出版日期:
2024-07-30

文章信息/Info

Title:
Progress in diagnosis and treatment of hemangioblastoma of the central nervous system
文章编号:
1009-153X（2024）07-0431-03
作者:
赵国杰; 刘仁忠
430060武汉，武汉大学人民医院神经外科（赵国杰、刘仁忠）
Author(s):
ZHAO Guo-jie;  LIU Ren-zhong
Department of Neurosurgery, Renmin Hospital of Wuhan University, Wuhan 430060, China
关键词:
血管母细胞瘤; 中枢神经系统; von Hippel-Lindau（VHL）病; 诊断; 治疗
Keywords:
Hemangioblastoma;  Central nervous system;  von Hippel-Lindau (VHL) disease;  Diagnosis;  Treatment
分类号:
R 739.41
DOI:
10.13798/j.issn.1009-153X.2024.07.010
文献标志码:
A
摘要:
血管母细胞瘤是一种较为罕见的中枢神经系统良性肿瘤。它既可散发，亦可作为von Hippel-Lindau（VHL）病的一部分出现，约占颅内肿瘤的2%，占原发性脊髓肿瘤的2%~10%。影像学检查是术前诊断血管母细胞瘤的重要手段，而最终确诊需要依赖于病理诊断。目前，血管母细胞瘤的主要治疗方法为显微手术，病死率较低，远期手术效果良好。近年来，随着研究的深入，临床对于血管母细胞瘤有了新的认识。本文就中枢神经系统血管母细胞瘤的诊治进展作一综述，为临床诊治血管母细胞瘤提供参考。
Abstract:
Hemangioblastoma is a relatively rare benign tumor of the central nervous system. It can occur sporadically or as part of von Hippel-Lindau (VHL) disease, accounting for approximately 2% of intracranial tumors and 2%~10% of primary spinal cord tumors. Imaging examinations are important means for preoperative diagnosis of hemangioblastoma, while the final diagnosis relies on pathological diagnosis. Currently, the main treatment for hemangioblastoma is microsurgery, which has a low mortality rate and favorable long-term surgical outcomes. In recent years, with in-depth research, there have been new insights into hemangioblastoma in clinical practice. This article presents a review of the progress in the diagnosis and treatment of hemangioblastoma of the central nervous system, providing a reference for the clinical diagnosis and treatment of hemangioblastoma.

参考文献/References:

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备注/Memo

备注/Memo:
（2022-09-24收稿，2024-03-16修回）
通信作者：刘仁忠，Email：lrz1961@163.com
更新日期/Last Update: 2024-07-30